Dramatic response of refractory sarcoidosis under ruxolitinib in a patient with associated JAK2-mutated polycythemia.
Identifieur interne : 000C40 ( Main/Exploration ); précédent : 000C39; suivant : 000C41Dramatic response of refractory sarcoidosis under ruxolitinib in a patient with associated JAK2-mutated polycythemia.
Auteurs : Cécile Rotenberg [France] ; Valérie Besnard [France] ; Pierre-Yves Brillet [France] ; Stéphane Giraudier [France] ; Hilario Nunes [France] ; Dominique Valeyre [France]Source :
- The European respiratory journal [ 1399-3003 ] ; 2018.
Descripteurs français
- KwdFr :
- Adulte d'âge moyen, Biopsie, Femelle, Hormones corticosurrénaliennes (usage thérapeutique), Humains, Hydroxychloroquine (usage thérapeutique), Kinase Janus-2 (génétique), Mutation, Polyglobulie primitive essentielle (génétique), Polyglobulie primitive essentielle (traitement médicamenteux), Pyrazoles (usage thérapeutique), Radiographie thoracique, Résultat thérapeutique, Sarcoïdose (génétique), Sarcoïdose (traitement médicamenteux), Tomodensitométrie, Transduction du signal.
- MESH :
- génétique : Kinase Janus-2, Polyglobulie primitive essentielle, Sarcoïdose.
- traitement médicamenteux : Polyglobulie primitive essentielle, Sarcoïdose.
- usage thérapeutique : Hormones corticosurrénaliennes, Hydroxychloroquine, Pyrazoles.
- Adulte d'âge moyen, Biopsie, Femelle, Humains, Mutation, Radiographie thoracique, Résultat thérapeutique, Tomodensitométrie, Transduction du signal.
English descriptors
- KwdEn :
- Adrenal Cortex Hormones (therapeutic use), Biopsy, Female, Humans, Hydroxychloroquine (therapeutic use), Janus Kinase 2 (genetics), Middle Aged, Mutation, Polycythemia Vera (drug therapy), Polycythemia Vera (genetics), Pyrazoles (therapeutic use), Radiography, Thoracic, Sarcoidosis (drug therapy), Sarcoidosis (genetics), Signal Transduction, Tomography, X-Ray Computed, Treatment Outcome.
- MESH :
- chemical , genetics : Janus Kinase 2.
- chemical , therapeutic use : Adrenal Cortex Hormones, Hydroxychloroquine, Pyrazoles.
- drug therapy : Polycythemia Vera, Sarcoidosis.
- genetics : Polycythemia Vera, Sarcoidosis.
- Biopsy, Female, Humans, Middle Aged, Mutation, Radiography, Thoracic, Signal Transduction, Tomography, X-Ray Computed, Treatment Outcome.
DOI: 10.1183/13993003.01482-2018
PubMed: 30361243
Affiliations:
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Le document en format XML
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